rdf-syntax-grammar
mods:
  schema location: http://www.loc.gov/mods/v3 http://www.loc.gov/standards/mods/v3/mods-3-2.xsd
  title info:
    title: Treatment of Cystic Fibrosis and Other Rare Lung Diseases
  name:
    name part: Azuma, Arata.
    role:
      role term: editor.
  name:
    name part: Schechter, Michael S.
    role:
      role term: editor.
  name:
    name part: SpringerLink (Online service)
  type of resource: text
  origin info:
    place:
      place term: sz
    date issued: 2017
    issuance: monographic
  language:
    language term: eng
  physical description:
    form: electronic
    form: electronic resource
    reformatting quality: access
    form: remote
    extent: VIII, 263 p. 33 illus., 14 illus. in color. online resource.
  abstract: This volume describes the pathogenesis and pathophysiology of several pulmonary diseases as well as their treatment. It also discusses the underlying genetic and molecular biological basis, which opens the way for new treatments for these conditions. It focuses on the treatment of cystic fibrosis including CFTR (cystic fibrosis transmembrane-conductance regulator) modulator therapies, drug therapies that augment airway surface liquid as well as anti-inflammatory and anti-infective therapies. Further topics include long-term, low-dose macrolide therapy for diffuse panbronchiolitis; novel agents for previously untreatable idiopathic pulmonary fibrosis; possible new treatments for pulmonary alveolar proteinosis (PAP); and multiple novel therapeutic targets for treating lymphangiomyomatosis. Research into these conditions has led to major advances in our understanding of the underlying genetic and molecular basis of this disease, and to dramatic improvements in survival and quality of life for affected individuals.
  table of contents: Part I Etiopathology and Genetics of Rare Lung Diseases -- Part II Treatment of Cystic Fibrosis -- Part III Treatment of Other Rare Lung Diseases.
  note: edited by Arata Azuma, Michael S. Schechter.
  subject:
    topic: Medicine
  subject:
    topic: Immunology
  subject:
    topic: Pharmacology
  subject:
    topic: Internal medicine
  subject:
    topic: Respiratory organs
    topic: Diseases
  subject:
    topic: Biomedicine
  subject:
    topic: Pharmacology/Toxicology
  subject:
    topic: Pneumology/Respiratory System
  subject:
    topic: Internal Medicine
  subject:
    topic: Immunology
  classification: RM1-950
  classification: 615
  related item:
    title info:
      title: Springer eBooks
  related item:
    title info:
      title: Milestones in Drug Therapy
  identifier: 9783034809771
  identifier: http://dx.doi.org/10.1007/978-3-0348-0977-1
  record info:
    record creation date: 170201
    record change date: 20170201181627.0
    record identifier: 978-3-0348-0977-1