Current Views of Fatty Acid Oxidation and Ketogenesis From Organelles to Point Mutations /

Λεπτομέρειες βιβλιογραφικής εγγραφής
Συγγραφή απο Οργανισμό/Αρχή: SpringerLink (Online service)
Άλλοι συγγραφείς: Quant, Patti A. (Επιμελητής έκδοσης), Eaton, Simon (Επιμελητής έκδοσης)
Μορφή: Ηλεκτρονική πηγή Ηλ. βιβλίο
Γλώσσα:English
Έκδοση: Boston, MA : Springer US, 2002.
Σειρά:Advances in Experimental Medicine and Biology, 466
Θέματα:
Διαθέσιμο Online:Full Text via HEAL-Link
Πίνακας περιεχομένων:
  • Biogenesis of the Rat Liver Mitochondrial Carnitine Palmitoyltransferase I
  • Subcellular Distributuon of Mitochondrial Carnitine Palmitoyltransferase I in Rat Liver
  • Topology of Hepatic Mitochondrial Carnitine Palmitoyltransferase I
  • Possible Involvement of Cytoskeletal Components in the Control of Hepatic Carnitine Palmitoyltransferase I Activity
  • Effects of 3-Thia Fatty Acids on ?-Oxidation and Carnitine Palmitoylatransferase I Activity in Cultured Rat Hepatocytes
  • Carnitine Acyltransferases and Associated Transport Processes in the Endoplasmic Reticulum
  • Reciprocal Enzymatic Interference of Carnitine Palmitoyltransferase I and Glycerol-3-Phosphate Acyltransferase in Purified Liver Mitochondria
  • Characterization of a Response Element for Peroxisomal Proliferator Activated Receptor (PPRE) in Human Muscle-type Carnitine Palmitoyltransferase I
  • Kinetic Investigation of Carnitine Palmitoyltransferases in Homogenates of Human Skeletal Muscle Using L-amino-Carnitine and Malonyl-CoA
  • Processing of Carnitine Octanoyl Transferase pre-mRNAs by cis and trans-splicing
  • Selective Modulation of Carnitine Long-chain Acyltransferase Activities
  • Confocal Laser Scanning Microscopy of Human Skin Fibroblasts Showing Transient Expression of a Green Fluorescent Carnitine Palmitoyltransferase 1 Fusion Protein
  • Carnitine Biosynthesis
  • Hypolipidemic 3-Thia Fatty Acids
  • Molecular Mechanisms of Fatty Acid ?-Oxidation Enzyme Catalysis
  • Control of Mitochondrial ?-Oxidation at the Levels of [NAD+]/[NADH] and CoA Acylation
  • Production and Export of Acylcarnitine Esters by Neonatal Rat Hepatocytes
  • Tissue Specific Differences in Intramitochondrial Control of ?-Oxidation
  • Endotoxin-Induced Changes in Very-Low-Density Lipoprotein and Myocardial Utilisation of Triacylglycerol from Abnormal VLDL in the Rat
  • Effect of Valproic Acid on the Expression of Acyl-CoA Dehydrogenases in Various Tissues
  • Formation of a Human “Electron Transferring Flavoprotein”
  • Cloning and Regulation of Peroxisome Proliferator-Induced Acyl-CoA Thioesterases From Mouse Liver
  • Metabolic Effects of 3-Thia Fatty Acid in Cancer Cells
  • Poorly Oxidizable Fatty Acid Analogues Inhibit the Proliferation of Cancer Cells in Culture
  • The Role of PPAR? as a“lipostat” Transcription Factor
  • The Hypolipidaemic Effect of EPA is Potentiated by 2- and 3-Methylation
  • Is it Time to Reconsider the Role of CPT I in Control of Hepatic Ketogenesis?
  • Developmental Comparison of Human and Rat Hepatic Mitochondrial 3-Hydroxy-3-Methylglutaryl-CoA Synthase
  • Regulation of the Ketogenic Enzyme Mitochondrial 3-Hydroxy-3-Methylglutaryl-COA Synthase in Astrocytes and Meningeal Fibroblasts
  • Studies on Regulation of the Peroxisomal ?-Oxidation at the 3-Ketothiolase Step
  • Role and Organization of Peroxisomal ?-Oxidation
  • Hepatic ?-Oxidation of Phytanic Acid
  • Functions and Dysfunctions of Peroxisomes in Fatty Acid ?- and ?-Oxidation
  • Enzymology of ?-Oxidation of (Poly)unsaturated Fatty Acids
  • The Effect of ?-Oxidable and Non-?-Oxidable Thia Fatty Acids on Fatty Acid Metabolism
  • EPA and DHA Possess Different Metabolic Properties
  • The Use of [9,10-3H]Myristate, [9,10-3H]Palmitate and [9,10-3H]Oleate for the Detection and Diagnosis of Medium and Long-Chain Fatty Acid Oxidation Disorders in Intact Cultured Fibroblasts
  • Rapid Diagnosis of Organic Acidemias and Fatty-acid Oxidation Defects by Quantitative Electrospray Tandem-MS Acyl-Carnitine Analysis in Plasma
  • Genetics of Carnitine Palmitoyltransferase II Deficiencies
  • Identification of a Missense Mutation in a Patient with Lethal Carnitine Acyl-Carnitine Carrier Deficiency
  • MCAD Deficiency
  • D-Hydroxyacyl-CoA Dehydrogenase Deficiency
  • Phytanoyl-CoA Hydroxylase Deficiency
  • Rationale for a Conditional Knockout Mouse Model to Study Carnitine Palmitoyltransferase I Deficiencies
  • Biochemical Characterisation of Mutations of Human Medium-Chain Acyl-CoA Dehydrogenase
  • Lessons Learned from The Mouse Model of Short-Chain Acyl-CoA Dehydrogenase Deficiency.