Fibrocystic Diseases of the Liver

• Corporate Author: SpringerLink (Online service)
• Other Authors: Murray, Karen F. (Editor), Larson, Anne M. (Editor)
• Format: Electronic eBook
• Language: English
• Published: Totowa, NJ : Humana Press, 2010.
• Series: Clinical Gastroenterology
• Subjects: Medicine.; Gastroenterology.; Hepatology.; Nephrology.; Pediatrics.; Abdominal surgery.; Medicine & Public Health.; Abdominal Surgery.

In recent years there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis,...

Table of Contents:

• Pathophysiology and Development
• Embryology and Development of the Ductal Plate
• Cholangiocyte Biology as Relevant to Cystic Liver Diseases
• Cholangiocyte Cilia and Basal Bodies
• Genetics of Fibrocystic Diseases of the Liver and Molecular Approaches to Therapy
• Diagnosis
• Radiologic Findings in the Fibrocystic Diseases
• Pathology of Fibrocystic Diseases of the Liver
• Disease States
• Alagille Syndrome and JAGGED1/NOTCH Sequence
• Biliary Atresia and the Ductal Plate
• Nephronophthisis and Renal–Hepatic–Pancreatic Dysplasia of Ivemark
• Meckel and Joubert Syndromes
• Bardet–Biedl and Jeune Syndromes
• Congenital Disorders of Glycosylation and Their Effects on the Liver
• Autosomal Recessive Polycystic Kidney Disease
• Caroli Disease, Caroli Syndrome, and Congenital Hepatic Fibrosis
• Simple Hepatic Cysts/Choledochal Cysts
• Autosomal Dominant Polycystic Liver Disease
• Echinococcal/Hydatid Cysts of the Liver
• Miscellaneous Cystic Lesions of the Liver
• Complications
• Vascular Complications of Fibrocystic Liver Disease
• Biliary Cystadenoma and Cystadenocarcinoma
• Cholangitis
• Surgical Management
• Surgical Management of Fibrocystic Liver Disease.