Congenital Diseases in the Right Heart

• Συγγραφή απο Οργανισμό/Αρχή: SpringerLink (Online service)
• Άλλοι συγγραφείς: Redington, Andrew N. (Επιμελητής έκδοσης), Arsdell, Glen S. Van (Επιμελητής έκδοσης), Anderson, Robert H. (Επιμελητής έκδοσης)
• Μορφή: Ηλεκτρονική πηγή Ηλ. βιβλίο
• Γλώσσα: English
• Έκδοση: London : Springer London, 2009.
• Θέματα: Medicine.; General practice (Medicine).; Internal medicine.; Cardiology.; Pediatrics.; Cardiac surgery.; Medicine & Public Health.; Internal Medicine.; Cardiac Surgery.; General Practice / Family Medicine.

 A decade ago the right heart had been ignored in terms of its functional contribution to the circulation in acquired and congenital heart disease. While it remains a popular characterization, our understanding of right heart hemodynamics and pathophysiology, and their contribution to cardiac disease has matured immensely. Congenital Diseases in the Right Heart is a timely addition to the literature and represents the state of the art in right heart disease, bringing together experts in the field from across the world. The mandate for each author was to produce a state of the art contribution. Consequently, this book takes the reader from the most recent findings regarding the embryologic origins of the right heart, to the most practical aspects of management of right heart disease in acquired and congenital heart anomalies. Nevertheless, the right heart is not covered to the exclusion of its left-sided counterpart. Indeed, the last ten years have taught us that the right heart cannot be described in isolation. There is virtually no aspect of cardiac anatomy, physiology or disease that is not influenced by biventricular interactions. The understanding and therapeutic modification of such interactions will be a challenge for scientists and clinicians over the next ten years. This text is a distillation of thought and expertise that will provide the reader with an unique resource in evaluating and managing patients with right heart disease. It will consequently be of great importance to all involved in this discipline, including pediatric cardiologists, cardiac surgeons, intensivists, cardiac pathologists and researchers in anatomy, embryology and cardiology. 

 Basic Topics -- Origin and Identity of the Right Heart -- How Much of the Right Heart Belongs to the Left? -- Right Ventricular Physiology -- The Pulmonary Vascular Bed -- Pulmonary Endothelial Control of the Pulmonary Microcirculation -- The Pathobiology of Pulmonary Hypertension: Lessons from Experimental Studies -- Pulmonary Arterial Hypertension: Genetics and Gene Therapy -- Imaging Pulmonary Microvascular Flow -- Functional Evaluation of Pulmonary Circulation: With Special Emphasis on Magnetic Resonance Imaging -- Transcatheter Intervention on the Central Pulmonary Arteries—Current Techniques and Outcomes -- Surgical Repair of Pulmonary Arterial Stenosis -- The Systemic Right Ventricle -- Mechanisms of Late Systemic Right Ventricular Failure -- Pharmacologic Approaches to the Failing Systemic Right Ventricle -- Congenitally Corrected Transposition: Replacement of the Tricuspid Valve or Double Switch? -- Disease in The Absence of Structural Malformations -- Right Ventricular Tachycardia -- Genetic Origins of Right Ventricular Cardiomyopathies -- The Pathology of Arrhythmogenic Right Ventricular Cardiomyopathy -- The Diagnosis of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) in Children -- Clinical Outcomes and Current Therapies in Arrhythmogenic Right Ventricular Cardiomyopathy -- The Small Right Ventricle -- Imaging the Hypoplastic Right Heart – How Small Is Too Small? -- The Small Right Ventricle—Who Should Get a Fontan? -- Surgery for the Small Right Ventricle -- The Right Ventricle on the Intensive Care Unit -- Postoperative Pulmonary Hypertension: Pathophysiology and Current Management Strategies -- Ventilatory Management of the Failing Right Heart -- Origins and Treatment of Right Ventricular Dysfunction After Heart Transplantation -- Noninvasive Assessment of Right Ventricular Contractile Performance -- Acute Right Ventricular Failure -- The Subpulmonary Right Ventricle in Chronic Left Ventricular Failure -- Tetralogy of Fallot -- Tetralogy of Fallot: Managing the Right Ventricular Outflow -- Restrictive Right Ventricular Physiology: Early and Late Effects -- Pulmonary Regurgitation in Relation to Pulmonary Artery Compliance and Other Variables -- Late Arrhythmia in Tetralogy of Fallot: Current Approaches to Risk Stratification -- Timing and Outcome of Surgical Pulmonary Valve Replacement -- Nonsurgical Replacement of the Pulmonary Valve -- Ebsteins Anomaly -- Anatomic Definition and Imaging of Ebstein’s Malformation -- Ebstein’s Anomaly of the Tricuspid Valve: Fetal Physiology and Outcomes -- Percutaneous Interatrial Defect Closure in Adults with Ebstein’s Anomaly -- Surgical Options for Ebstein’s Malformation -- Special Topics -- The Role of Resynchronization Therapy in Congenital Heart Disease: Right–Left Heart Interactions -- Causes of Failure of the Fontan Circulation.