Humoral Primary Immunodeficiencies

• Συγγραφή απο Οργανισμό/Αρχή: SpringerLink (Online service)
• Άλλοι συγγραφείς: D'Elios, Mario Milco (Επιμελητής έκδοσης, http://id.loc.gov/vocabulary/relators/edt), Rizzi, Marta (Επιμελητής έκδοσης, http://id.loc.gov/vocabulary/relators/edt)
• Μορφή: Ηλεκτρονική πηγή Ηλ. βιβλίο
• Γλώσσα: English
• Έκδοση: Cham : Springer International Publishing : Imprint: Springer, 2019.
• Έκδοση: 1st ed. 2019.
• Σειρά: Rare Diseases of the Immune System,
• Θέματα: Rheumatology.; Immunology.; Infectious diseases.; Oncology .; Infectious Diseases.; Oncology.

This book presents detailed state of the art knowledge on the humoral primary immunodeficiencies (PIDs), i.e., disorders arising from impaired antibody production due to defects intrinsic to B cells or defective interaction between B and T cells. There is extensive coverage of both basic science dis...

Πίνακας περιεχομένων:

• Preface
• 1. B cells and the B-cell immunological synapse.-2 Mucosal B cells
• 3 CVID. - 4 LOCID. - 5 Genetics of CVID. - 6 ICOS deficiency. - 7 CD19 deficiency
• 8 CD20 deficiency. - 9 CD21 deficiency. - 10 CD81 deficiency. - 11 TACI deficiency, . - 12 LRBA deficiency. - 13 BAFF receptor deficiency. - 14 TWEAK defects. - 15 NFKB2 deficiency. - 16 WHIM syndrome. - 17 Novel humoral PID genes. - 18 Class Switch Recombination defects,
• 19 Selective IgA deficiency
• 20 IgA with IgG subclass deficiency. - 21 Isolated IgG subclass deficiency. - 22 Thymoma with immunodeficiency. - 23 PRKC delta and PI3K-delta associated diseases. - 24 Differential diagnostic in hypogammaglobulinemia. - 25 Management of Humoral primary immunodeficiencies in pediatrics
• 26 Management of Humoral primary immunodeficiencies in adults
• 27 Vaccines in humoral PID
• 28 Humoral PID and neoplasias
• 29 Humoral PID and autoimmunity. - 30 Lung involvement
• 31 Gut involvement
• Subject Index.