Primary Immunodeficiency Diseases Definition, Diagnosis, and Management /

• Corporate Author: SpringerLink (Online service)
• Other Authors: Rezaei, Nima (Editor), Aghamohammadi, Asghar (Editor), Notarangelo, Luigi D. (Editor)
• Format: Electronic eBook
• Language: English
• Published: Berlin, Heidelberg : Springer Berlin Heidelberg, 2008.
• Subjects: Medicine.; Human genetics.; Immunology.; Allergy.; Internal medicine.; Infectious diseases.; Pediatrics.; Medicine & Public Health.; Infectious Diseases.; Allergology.; Internal Medicine.; Human Genetics.

Primary immunodeficiency diseases (PID) are a group of disorders involving defects in one or more components of the immune system, and are characterized by an increased incidence of infections, autoimmunity, and malignancies. Although PID seem to be rare, the number of patients diagnosed has increas...

Table of Contents:

• An Introduction to Primary Immunodeficiency Diseases
• Combined T and B Cell Immunodeficiencies
• Predominantly Antibody Deficiencies
• Phagocytes Defects
• Genetic Disorders of Immune Regulation
• Defects in Innate Immunity: Receptors and Signaling Components
• Autoinflammatory Disorders
• Complement Deficiencies
• Other Well-Defined Immunodeficiencies
• Syndromic Immunodeficiencies
• Treatment of Primary Immunodeficiency Diseases.